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Khirurgii

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Year 2007 Vol. 15 No 4

LECTURES, REVIEWS

SPINDZHUK M.V., ADZERIKHO I.E., DERGACHOV A.V.

ABSTAIN ANOMALY

The definition, history, statistic data, etiology, anatomy and pathophysiology, clinical manifestation, diagnostics and treatment principles of the congenital cyanotic heart disease – Abstain anomaly - are briefly described in the article. Treatment tactics of Abstain anomaly is determined by the acuteness degree of the disease itself and influences of accompanying structural and electropathophysiological anomalies. From the medicinal preparations antibiotics are used to prevent infectious endocarditis as well as diuretics, inhibitors of angiotensin converting enzyme and digoxin for the treatment of cardiac insufficiency.
Indications for the surgical treatment are:
1) NYHA class III-VI;
2) significant or progressing cyanosis;
3) reduced tolerance to the physical exercises;
4) significant decrease in the growth graphic curve;
5) acute cardiomegaly (index more than 0, 65);
6) associated cardiac anomalies, including the right ventricle portion obstruction;
7) refractory ventricle and auricle arrhythmias;
8) paradoxical embolism in anamnesis.
Surgical treatment of the anomaly is aimed to prevent intracardiac shunting from the left to the right, to limit cardiomyopathy, to improve tolerance to the physical exercises and functional class. Surgery may be performed in one or more stages.

Keywords: Abstain anomaly, tricuspid insufficiency, congenital heart disease.
p. 112 - 122 of the original issue
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